June 6th, 2020

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Rare Coexistence of Mayer-Rokitansky-Küster-Hauser Syndrome and Ovarian Tumor of Low Malignant Potential in a Young Woman: A Case Report
Authors:  Zhimin Hao, M.D., and Sufen Yang, M.D.
BACKGROUND: Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome is characterized by varying degrees of uterovaginal aplasia. However, patients with MRKH syndrome have normal and functional ovaries.

CASE: An 18-year-old female patient previously diagnosed with MRKH syndrome presented with an abnormal mass on routine ultrasound examination; the mass was found to be an ovarian tumor of low malignant potential.

CONCLUSION: The development of ovarian tumor of low malignant potential combined with MRKH syndrome, although rare, is possible even in young patients and should be managed at an early stage.
Keywords:  borderline ovarian tumor, Mayer-Rokitansky-Küster-Hauser syndrome, Müllerian agenesis, ovarian tumor, ovary, uterine agenesis, vaginal agenesis
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